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2009 ; 9
(ä): 1031-4
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Unusual case report of thrombotic microangiopathy of the small bowel following
liver transplantation, a possible immunosuppressant-induced disease with
histological and ultrastructural findings
#MMPMID19802497
Piscitelli D
; Fiore MG
; Rossi R
; Casiello M
; Sanguedolce F
ScientificWorldJournal
2009[Oct]; 9
(ä): 1031-4
PMID19802497
show ga
Cyclosporin-A (CsA) and tacrolimus (FK-506) are immunomodulating agents used to
prevent rejection in organ transplantation. They are both associated with several
side effects, including nephrotoxicity and severe hypertension due to vascular
injury, which often appears as a microvascular occlusive disorder (thrombotic
microangiopathy, TMA). We report the first case of a microvascular occlusive
disorder with the features of TMA in the small bowel of an orthotopic liver
transplant (OLT) patient after immunosuppressive therapy with CsA and FK506. The
patient presented with severe recurrent abdominal colics and distal subocclusion,
requiring aggressive surgical treatment. Histological and ultrastructural
analysis of the resected specimen disclosed intestinal TMA. Although rare, such a
complication should be considered in the differential diagnosis of abdominal
colics in patients undergoing immunosuppressant therapy after OLT.