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2017 ; 56
(12
): 1575-1580
Nephropedia Template TP
gab.com Text
Twit Text FOAVip
Twit Text #
English Wikipedia
Efficacy of Intravenous Cyclophosphamide Pulse Therapy for
P-Glycoprotein-expressing B Cell-associated Active True Renal Lupus Vasculitis in
Lupus Nephritis
#MMPMID28626187
Kawabe A
; Tsujimura S
; Saito K
; Tanaka Y
Intern Med
2017[]; 56
(12
): 1575-1580
PMID28626187
show ga
True renal lupus vasculitis (TRLV), a vascular lesion usually associated with
proliferative lupus nephritis (LN), is resistant to conventional treatments. The
expression of P-glycoprotein (P-gp) on activated lymphocytes causes drug
resistance. We herein report a patient with TRLV, minimal change LN,
overexpression of P-gp on peripheral B cells, and accumulation of P-gp(+) B cells
at the site of TRLV. High-dose corticosteroids combined with intravenous
cyclophosphamide pulse therapy resulted in clinical remission and the long-term
normal renal function.
|ATP Binding Cassette Transporter, Subfamily B, Member 1/biosynthesis
[MESH]
|B-Lymphocytes/metabolism
[MESH]
|Cyclophosphamide/administration & dosage/*therapeutic use
[MESH]
|Drug Administration Schedule
[MESH]
|Female
[MESH]
|Humans
[MESH]
|Immunosuppressive Agents/administration & dosage/*therapeutic use
[MESH]