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Deprecated: Implicit conversion from float 233.6 to int loses precision in C:\Inetpub\vhosts\kidney.de\httpdocs\pget.php on line 534 J+Cell+Biol 2017 ; 216 (5): 1301-20 Nephropedia Template TP
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The BEACH-containing protein WDR81 coordinates p62 and LC3C to promote aggrephagy #MMPMID28404643
Liu X; Li Y; Wang X; Xing R; Liu K; Gan Q; Tang C; Gao Z; Jian Y; Luo S; Guo W; Yang C
J Cell Biol 2017[May]; 216 (5): 1301-20 PMID28404643show ga
Mutations in WDR81, a regulator of the endosomal?lysosomal pathway, are implicated in CAMRQ2 syndrome, which manifests as cerebellar ataxia, mental retardation, and quadrupedal locomotion in patients. In this study, Liu et al. uncover a distinct function of WDR81 in the clearance of ubiquitinated and aggregated proteins by autophagy.