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2013 ; 2
(2
): 144-147
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English Wikipedia
AP-VAS 2012 case report: a case of myeloperoxidase antineutrophil cytoplasmic
antibody-positive microscopic polyangiitis with rapidly progressive
glomerulonephritis and hearing loss
#MMPMID28509284
Tsukamoto M
; Shimizu S
; Koizumi M
; Kitahara N
; Ohtaki Y
; Aoki S
; Miyakawa H
CEN Case Rep
2013[Nov]; 2
(2
): 144-147
PMID28509284
show ga
A 74-year-old Japanese woman was admitted to our hospital because of fever,
fatigue, and hearing loss associated with vertigo. She had a 1-year history of
hearing impairment that got worse gradually and had been treated as otitis media
with effusion, but without remarkable improvement. After admission, she developed
renal dysfunction associated with hematuria and proteinuria. Laboratory tests
showed leukocytosis and elevated C-reactive protein. Myeloperoxidase
antineutrophil cytoplasmic antibody (MPO-ANCA) was elevated, but proteinase-3
antineutrophil cytoplasmic antibody (PR3-ANCA) was negative. Renal biopsy
revealed pauci-immune focal necrotizing glomerulonephritis with crescents. She
was diagnosed as having MPO-ANCA-associated polyangiitis. After treatment with
500 mg methylprednisolone applied intravenously for 3 days, followed by 40 mg
prednisolone administered orally, renal function recovered completely. Her
hearing also improved. Although otolaryngological symptoms are common in PR3-ANCA
associated vasculitis, hearing loss is a rare manifestation of MPO-ANCA
associated vasculitis (MPO-AAV). Our case suggests that AAV should be considered
in the differential diagnosis of hearing loss.