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2017 ; 4
(1
): 70-72
Nephropedia Template TP
gab.com Text
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English Wikipedia
Refractory optic perineuritis due to granulomatosis with polyangiitis
successfully treated with methotrexate and mycophenolate mofetil combination
therapy
#MMPMID28293459
Kimura Y
; Asako K
; Kikuchi H
; Kono H
Eur J Rheumatol
2017[Mar]; 4
(1
): 70-72
PMID28293459
show ga
Optic perineuritis is an uncommon inflammatory disorder of the optic sheath that
causes visual loss or eye pain. There are few case reports of optic perineuritis
associated with granulomatosis with polyangiitis. Herein we report the case of a
37-year-old male with granulomatosis with polyangiitis and who presented with
headache, blurred vision in the right eye, diplopia, and numbness in the right
forehead. Brain magnetic resonance images (MRI) findings revealed hypertrophic
pachymeningitis and refractory optic perineuritis. These were manageable only by
means of weekly methotrexate and mycophenolate mofetil combination therapy but
not with methotrexate, mycophenolate mofetil, intravenous cyclophosphamide,
rituximab, azathioprine, or cyclosporine individually.