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.jpg): Failed to open stream: No such file or directory in C:\Inetpub\vhosts\kidney.de\httpdocs\pget.php on line 117 Mediterr+J+Hematol+Infect+Dis
2016 ; 8
(1
): e2016053
Nephropedia Template TP
gab.com Text
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English Wikipedia
Hyperhemolytic Syndrome Complicating a Delayed Hemolytic Transfusion Reaction due
to anti-P1 Alloimmunization, in a Pregnant Woman with HbO-Arab/?-Thalassemia
#MMPMID27872733
Bezirgiannidou Z
; Christoforidou A
; Kontekaki E
; Anastasiadis AG
; Papamichos SI
; Menexidou H
; Margaritis D
; Martinis G
; Mantadakis E
Mediterr J Hematol Infect Dis
2016[]; 8
(1
): e2016053
PMID27872733
show ga
BACKGROUND: Hyperhemolytic Syndrome or Hyperhemolytic Transfusion Reaction
(HHTR), a life-threatening subset of Delayed Hemolytic Transfusion Reaction
(DHTR) is characterized by destruction of both transfused and autologous
erythrocytes evidenced by a fall in post transfusion hemoglobin below the
pre-transfusion level. CASE REPORT: We describe a case of DHTR due to anti-P1
alloimmunization manifesting with hyperhemolysis in a 30-year-old Greek Pomak
woman with thalassemia intermedia (HbO-Arab/?-thalassemia), during the11(th) week
of her first gestation. She was successfully managed with avoidance of further
transfusions and administration of IVIG and corticosteroids. CONCLUSION: A high
index of suspicion for HHTR is of vital importance among clinicians especially
since optimal methods for its prevention and treatment remain yet to be defined.
Early recognition of HHTR leading to prompt cessation of additional transfusions
and initiation of immunosuppressive treatment can be life-saving, especially in
clinical settings where limited therapeutic options are available, such as in
pregnancy.