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2016 ; 95
(16
): e3374
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Decreased ADAMTS 13 Activity is Associated With Disease Severity and Outcome in
Pediatric Severe Sepsis
#MMPMID27100422
Lin JJ
; Chan OW
; Hsiao HJ
; Wang Y
; Hsia SH
; Chiu CH
Medicine (Baltimore)
2016[Apr]; 95
(16
): e3374
PMID27100422
show ga
Decreased ADAMTS 13 activity has been reported in severe sepsis and in
sepsis-induced disseminated intravascular coagulation. This study aimed to
investigate the role of ADAMTS 13 in different pediatric sepsis syndromes and
evaluate its relationship with disease severity and outcome. We prospectively
collected cases of sepsis treated in a pediatric intensive care unit, between
July 2012 and June 2014 in Chang Gung Children's Hospital in Taoyuan, Taiwan.
Clinical characteristics and ADAMTS-13 activity were analyzed. All sepsis
syndromes had decreased ADAMTS 13 activity on days 1 and 3 of admission compared
to healthy controls. Patients with septic shock had significantly decreased
ADAMTS 13 activity on days 1 and 3 compared to those with sepsis and severe
sepsis. There was a significant negative correlation between ADAMTS 13 activity
on day 1 and day 1 PRISM-II, PELOD, P-MOD, and DIC scores. Patients with
mortality had significantly decreased ADAMTS 13 activity on day 1 than survivors,
but not on day 3. Different pediatric sepsis syndromes have varying degrees of
decreased ADAMTS 13 activity. ADAMTS 13 activity is strongly negatively
correlated with disease severity of pediatric sepsis syndrome, whereas decreased
ADAMTS 13 activity on day 1 is associated with increased risk of mortality.