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2015 ; 90
(6
): 892-5
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English Wikipedia
Granulomatous slack skin T-cell lymphoma: an important differential diagnosis
with giant cell tumor of soft tissue
#MMPMID26734874
Adriano AR
; Lima TS
; Battistella M
; Bagot M
An Bras Dermatol
2015[Nov]; 90
(6
): 892-5
PMID26734874
show ga
Granulomatous slack skin is an indolent T-cell lymphoma, considered to be a
variant of mycosis fungoides. Clinically it is characterized by areas of
redundant skin, wrinkled, inelastic, with variable erythema and infiltration
besides a poikilodermic surface. A differential diagnosis unknown to most
dermatologists is the giant cell tumor of soft tissue, which is an extremely rare
low-grade sarcoma. The authors report a patient who had undergone extensive
surgery because of a primary diagnosis of giant cell tumor of soft tissue, but
which proved to be granulomatous slack skin after a second interventional
procedure with confirmatory histopathology.