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2015 ; 2015
(ä): ä Nephropedia Template TP
gab.com Text
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Twit Text #
English Wikipedia
A rare case of bilateral cystic partially differentiated nephroblastoma recurring
as bilateral cystic Wilms tumour
#MMPMID25878237
Kurian JJ
; Ninan PJ
BMJ Case Rep
2015[Apr]; 2015
(ä): ä PMID25878237
show ga
Childhood cystic partially differentiated nephroblastoma (CPDN) is an uncommon
renal neoplasm. Bilateral CPDN or CPDN co-existing with a cystic nephroma/Wilms
tumour is extremely rare. Treatment of CPDN is by complete surgical excision.
Although local recurrences are uncommon, distant metastases have not been
described. We present a case of bilateral CPDN that, after complete excision,
recurred as bilateral cystic Wilms tumour. To the best of our knowledge, this is
the first reported case in the literature where a bilateral CPDN has recurred as
bilateral Wilms tumour.