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2014 ; 23
(9
): 898-904
Nephropedia Template TP
gab.com Text
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Twit Text #
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Comparison of renal response parameters for juvenile membranous plus
proliferative lupus nephritis versus isolated proliferative lupus nephritis: a
cross-sectional analysis of the CARRA Registry
#MMPMID24729278
Boneparth A
; Ilowite NT
Lupus
2014[Aug]; 23
(9
): 898-904
PMID24729278
show ga
Lupus nephritis (LN) affects many patients with juvenile systemic lupus
erythematosus (SLE) and is a significant cause of disease morbidity. Membranous
plus proliferative LN (M?+?PLN) may represent a more difficult to treat subtype
of juvenile LN, compared to isolated proliferative LN (PLN). In this
retrospective observational study, we utilized data from the Childhood Arthritis
and Rheumatism Research Alliance (CARRA) registry to compare response rates for
pediatric M?+?PLN versus PLN. Response was assessed at the most recent CARRA
registry visit gathered ?6 months after diagnostic kidney biopsy. Estimated
glomerular filtration rate (GFR) less than 90?ml/min/1.73?m(2), indicating renal
insufficiency, was found in 16.1% of patients with M?+?PLN and 6.1% of patients
with PLN (P?=?0.071). We found no significant difference in achievement of
response in either hematuria or proteinuria between PLN and M?+?PLN groups or
between subgroups determined by presence of class III vs. class IV proliferative
disease. Exposure rates to mycophenolate, cyclophosphamide, and rituximab were
similar between groups. Future studies will be necessary to correlate pediatric
LN renal histology data with treatment response as well as other disease outcome
measures.