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2013 ; 2013
(ä): 324315
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Glomerular disease in patients with infectious processes developing
antineutrophil cytoplasmic antibodies
#MMPMID24959541
Konstantinov KN
; Emil SN
; Barry M
; Kellie S
; Tzamaloukas AH
ISRN Nephrol
2013[]; 2013
(ä): 324315
PMID24959541
show ga
To identify differences in treatment and outcome of various types of
glomerulonephritis developing in the course of infections triggering
antineutrophil cytoplasmic antibody (ANCA) formation, we analyzed published
reports of 50 patients. Immunosuppressives were added to antibiotics in 22 of 23
patients with pauci-immune glomerulonephritis. Improvement was noted in 85% of 20
patients with information on outcomes. Death rate was 13%. Corticosteroids were
added to antibiotics in about 50% of 19 patients with postinfectious
glomerulonephritis. Improvement rate was 74%, and death rate was 26%. Two
patients with mixed histological features were analyzed under both pauci-immune
and post-infectious glomerulonephritis categories. In 9 patients with other renal
histology, treatment consisted of antibiotics alone (7 patients), antibiotics
plus immunosuppressives (1 patient), or immunosuppressives alone (1 patient).
Improvement rate was 67%, permanent renal failure rate was 22%, and death rate
was 11%. One patient with antiglomerular basement disease glomerulonephritis
required maintenance hemodialysis. Glomerulonephritis developing in patients who
became ANCA-positive during the course of an infection is associated with
significant mortality. The histological type of the glomerulonephritis guides the
choice of treatment. Pauci-immune glomerulonephritis is usually treated with
addition of immunosuppressives to antibiotics.