A?Z of malignant peripheral nerve sheath tumors #MMPMID23108260
Kamran S; Shinagare A; Howard S; Hornick J; Ramaiya N
Cancer Imaging 2012[]; 12 (3): 473-83 PMID23108260show ga
This article reviews the typical and atypical locations, imaging findings, local recurrence, and metastatic pattern of malignant peripheral nerve sheath tumors (MPNSTs). MPNSTs are rare soft tissue sarcomas, commonly occur in extremities, and are often associated with neurofibromatosis. Distinction between benign and malignant tumors can be challenging on imaging. MPNSTs have a poor prognosis; however, rhabdomyoblastic differentiation (malignant triton tumor), which has imaging features similar to MPNSTs, is associated with even more aggressive behavior.