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2025 ; 19
(1
): 536
Nephropedia Template TP
gab.com Text
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English Wikipedia
Splenic artery embolization in a patient with advanced Caroli s syndrome
complicated by portal hypertension: a case report
#MMPMID41131542
Zohud A
; Akram M
; Khamaise Y
; Khamaise A
; Abdoh Q
J Med Case Rep
2025[Oct]; 19
(1
): 536
PMID41131542
show ga
BACKGROUND: Caroli's disease is an inherited disorder characterized by dilatation
of intrahepatic bile ducts and congenital hepatic fibrosis. Caroli's disease is
complicated by choledocholithiasis, cholangitis, and portal hypertension. CASE
PRESENTATION: A 28-year-old Palestinian female with 7-year history of Caroli's
disease complicated by liver cirrhosis, portal hypertension, and esophageal
varices presented with hypersplenism and thrombocytopenia. She was managed with
splenic artery embolization, which improved her platelet count. The splenic
artery embolization was complicated by postembolization syndrome, and she was
treated with antibiotics and supportive care. Two months later, she died owing to
liver encephalopathy and spontaneous bacterial peritonitis. CONCLUSION: This case
highlights the role of splenic artery embolization in managing hypersplenism
associated with Caroli's disease. Despite improvement in platelet count,
post-embolization syndrome remains a significant risk. Early liver
transplantation should be considered in patients with advanced Caroli's syndrome
to improve long-term outcomes.