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.jpg): Failed to open stream: No such file or directory in C:\Inetpub\vhosts\kidney.de\httpdocs\pget.php on line 117 Proc+(Bayl+Univ+Med+Cent)
2017 ; 30
(2
): 205-208
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Primitive neuroectodermal tumors of the kidney
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Narayanan G
; Rajan V
; Preethi TR
Proc (Bayl Univ Med Cent)
2017[Apr]; 30
(2
): 205-208
PMID28405084
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Ewing's sarcoma/primitive neuroectodermal tumor (ES/PNET) rarely occurs as a
primary renal tumor. The disease affects young adults and children and has an
aggressive course. The clinical presentation and imaging of these tumors are
nonspecific, and they often present at an advanced stage. We present the clinical
features, imaging, diagnosis, and treatment of 7 cases of renal PNET (4 men, 3
women; median age, 32 years). Common presenting symptoms were flank or abdominal
pain and a mass in the abdomen. On imaging, a large heterogenous infiltrating
renal mass with areas of calcification, hemorrhage, and necrosis and tumor
thrombus can give a clue to the diagnosis of renal PNET. Immunohistochemistry and
molecular studies are essential to confirm the diagnosis. The prognosis of renal
ES/PNET is generally poor. Radical nephrectomy combined with chemotherapy and
radiotherapy is the standard treatment for renal PNET. An early and accurate
diagnosis is crucial for the proper management of these aggressive tumors.
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