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10.1016/j.ccm.2016.04.012 http://scihub22266oqcxt.onion/10.1016/j.ccm.2016.04.012 C4987498!4987498 !27514596     free     free     free Warning: imagejpeg(C:\Inetpub\vhosts\kidney.de\httpdocs\phplern\27514596 .jpg): Failed to open stream: No such file or directory in C:\Inetpub\vhosts\kidney.de\httpdocs\pget.php on line 117       Clin+Chest+Med 2016 ; 37 (3 ): 505-11 Nephropedia Template TP {{tp|p=27514596 |t=2016. Hermansky-Pudlak Syndrome |pdf=|usr=}}{{27514596 }} gab.com Text Hermansky-Pudlak Syndrome JO: Clin Chest Med http://www.kidney.de/pget.php?&tw=1&pmid=27514596 #FOAvip Hermansky-Pudlak syndrome (HPS) is an autosomal recessive disorder that is associated with oculocutaneous albinism, bleeding diatheses, granulomatous colitis, and highly penetrant pulmonary fibrosis in some subtypes, including HPS-1, HPS-2, and HPS-4. HPS pulmonary fibrosis shows many of the clinical, radiologic, and histologic features found in idiopathic pulmonary fibrosis, but occurs at a younger age. Despite knowledge of the underlying genetic defects, there are currently no definitive therapeutic or preventive approaches for HPS pulmonary fibrosis other than lung transplant. Twit Text FOAVip Hermansky-Pudlak Syndrome ????Clin Chest Med http://www.kidney.de/pget.php?&tw=1&pmid=27514596 #FOAvip Twit Text # Free Paper on # # # # # LINK http://www.kidney.de/pget.php?&tw=1&pmid=27514596 #FOAvip English Wikipedia <ref>{{Cite pmid|27514596 }}</ref> Hermansky-Pudlak Syndrome #MMPMID27514596 El-Chemaly S ; Young LR Clin Chest Med 2016[Sep]; 37 (3 ): 505-11 PMID27514596 show ga Hermansky-Pudlak syndrome (HPS) is an autosomal recessive disorder that is associated with oculocutaneous albinism, bleeding diatheses, granulomatous colitis, and highly penetrant pulmonary fibrosis in some subtypes, including HPS-1, HPS-2, and HPS-4. HPS pulmonary fibrosis shows many of the clinical, radiologic, and histologic features found in idiopathic pulmonary fibrosis, but occurs at a younger age. Despite knowledge of the underlying genetic defects, there are currently no definitive therapeutic or preventive approaches for HPS pulmonary fibrosis other than lung transplant. |Albinism, Oculocutaneous/etiology/physiopathology [MESH] |Albinism/complications/physiopathology [MESH] |Arteriovenous Malformations/etiology/*physiopathology [MESH] |Blood Coagulation Disorders/etiology/*physiopathology [MESH] |Crohn Disease/etiology/physiopathology [MESH] |Epistaxis/etiology/physiopathology [MESH] |Gastrointestinal Diseases/etiology/physiopathology [MESH] |Hemorrhagic Disorders/complications/physiopathology [MESH] |Hermanski-Pudlak Syndrome/complications/*physiopathology [MESH] |Humans [MESH] |Hypertension, Pulmonary/etiology/*physiopathology [MESH] |Intracranial Arteriovenous Malformations/etiology/*physiopathology [MESH] |Liver Diseases/etiology/physiopathology [MESH] |Pulmonary Artery/abnormalities [MESH] |Pulmonary Fibrosis/etiology/*physiopathology [MESH] |Pulmonary Veins/abnormalities [MESH]Hermansky-Pudlak Syndrome (epmc).pdf DeepDyve Pubget Overpricing